An UNUSUAL CASE OF RESIDUAL FOLLICULAR LYMPHOMA WITH HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS.
Abstract
Follicular lymphoma is an indolent B-cell lymphoproliferative disorder of transformed follicular centre B cells characterised by diffuse lymphadenopathy, bone marrow involvement and splenomegaly. An uncommon, fatal clinical disease known as hemophagocytic lymphohistiocytosis is marked by hyperinflammation. HLH is brought on by abnormally activated macrophages and cytotoxic T cells, which produce acute organ dysfunction and cytokine storm. HLH caused by lymphoma is a rare but devastating condition. A rapid diagnosis will aid in effective treatment. This is a rare case report highlighting diagnosis and treatment plan of a 60 year old female patient with residual follicular lymphoma with hemophagocytic lymphohistiocytosis.
Keywords: follicular, lymphoma, hemophagocytic lymphohistiocytosis,
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References
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